Management of Connective Tissue Interstitial Lung Disease

Title:Management of Connective Tissue Interstitial Lung Disease

Volume: 11 Issue: 2

Author(s): Tracy M. Frech and Mary Beth Scholand

Affiliation:

Keywords: Collagen vascular disease, connective tissue disease, immunosuppressive therapy, interstitial lung disease, oxygen, pulmonary rehabilitation, supportive care.

Abstract: The connective tissue diseases (CTD) are frequently associated with Interestitial lung diseases (ILD). The presence of an ILD in a patient with CTD is associated with a higher morbidity and mortality. Management of a patient with connective tissue interstitial lung disease (CTD-ILD) depends on disease severity with a focus on improving quality of life. Therapeutic interventions include medications, which aim to prevent progression to fibrosis and decrease inflammation or alveolitis, supplemental oxygen; and pulmonary rehabilitation. Comorbidities including gastroesophageal reflux disease (GERD) and obstructive sleep apnea should be addressed in all CTD-ILD patients. Appropriate referral to support groups, lung transplantation centers, and palliative care are considerations for all patients with CTDILD. The management of a patient with CTD-ILD is a multidisciplinary personalized process that is driven by the specific disease, clinical pattern, and associated comorbidities.

Cite this article as:

Frech M. Tracy and Scholand Beth Mary, Management of Connective Tissue Interstitial Lung Disease, Current Respiratory Medicine Reviews 2015; 11 (2) . https://dx.doi.org/10.2174/1573398X11666150619183704