Abstract
OHVIRA syndrome, is a rare in-utero developmental defect affecting the female urogenital system, classically described as obstructed hemivagina and ipsilateral renal anomaly. Majority of the patients have clinical presentations of abdominal or pelvic pain, usually shortly post-menarche. Early detection and prompt treatment relieve symptoms and prevent complications. Similar presentations may be due to other entity of Mullerian abnormalities associated with single renal agenesis. Three cases illustrating the clinical presentations, the dilemma in achieving diagnosis and the treatment advocated for the patients. Case 1 is a classic OHVIRA syndrome while the other 2 cases are variants of the classic syndrome; the second case showed a contralateral renal agenesis and the third case had variants of Mullerian anomaly. High index of suspicion can help in the diagnosis of this rare OHVIRA syndrome, and there are possibilities of discovering new rare syndromes yet to be named.
Keywords: Mullerian duct anomaly, obstructed hemivagina, OHVIRA, uterine didelphy, vaginoplasty.
Call for Papers in Thematic Issues
RARE CASES IN GYNECOLOGY-OBSTETRICS
With the development of diagnostic and therapeutic techniques (such as ART techniques) and the immersion of new pathologies (such as COVID19), we are witnessing an increase in the incidence of pathologies that were previously described as rare or exceptional. the practitioner sometimes confronts difficult situations in these cases in diagnostic ...read more
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