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New Emirates Medical Journal

ISSN (Online): 0250-6882

Case Report

Methemoglobinaemia in Diabetic Ketoacidosis Patient

Author(s): Magdy Mohamed* and Nadem Javed

Volume 3, Issue 1, 2022

Published on: 27 December, 2021

Article ID: e290922199526 Pages: 3

DOI: 10.2174/03666211227181618

open access plus


Background: Glucose-6-phosphate dehydrogenase (G6PD) deficiency is a common X-linked genetic disorder.

Case Presentation: In this paper, we report a case of a 41-years-old male patient with non-insulin-dependent diabetes and a family history of G6PD deficiency never known to have any previous hemolytic episodes, presented as a case of diabetic ketoacidosis with features of hemolytic anemia due to G6PD deficiency manifesting as methemoglobinemia and anemia.

Conclusion: Our patient successfully managed with ascorbic acid and red blood cell transfusion. Clinicians should, therefore, be aware of the possibility of this uncommon association between diabetic ketoacidosis, G6PD deficiency, and methemoglobinemia which may be present in patients with G6PD deficiency and severe hemolysis.

Keywords: Case report, G6PD deficiency, Hemolysis, Methemoglobinemia, Diabetic ketoacidosis, Methylene blue, Vitamin C.

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