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New Emirates Medical Journal

Editor-in-Chief

ISSN (Print): -
ISSN (Online): 0250-6882

Case Report

An Aortic “Supravalvular Shelf” is Not Always Innocuous

Author(s): Laszlo Göbölös*, Gurjyot Bajwa, Jehad Ramahi, Pier Carlo Bergonzi and Gopal Bhatnagar

Volume 1 , Issue 1 , 2020

Page: [17 - 19] Pages: 3

DOI: 10.2174/0250688202002021101

open access plus

Abstract

Supravalvular aortic stenosis is a rare cause of secondary aortic root distension and/or aortic valve regurgitation. Non-syndromic aortic aneurysms may also occur in young adults and can develop silently, representing an asymptomatic, life-threatening condition. Clinicians should, therefore, be alert to the possibility of this uncommon, but potentially serious disease, often first revealed by an imaging modality requested for other indications, even in case of an established, more benign diagnosis.

Keywords: Aortic valve, Supravalvular membrane, Chronic, Aortic dissection, Aortic root, Pathological changes.

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