Background: Mounier Kuhn Syndrome (MKS) is a rare congenital anomaly characterized
by abnormal dilatation of the trachea and main bronchi. The aim of this study is to discuss tracheal
volume measurement in MKS, and the pathologies accompanying MKS, especially pulmonary
Materials and Methods: 38 patients, 18 of whom were diagnosed with MKS and 20 as control
group, were included in the study. Trachea volume and pulmonary artery diameter were measured
through thorax-computed tomography (CT) images of the patients. Accompanying pathologies
Results: In the measurements done through the CT scans, the trachea volume was found to be
25.45 cm3 in the control group and 44.17 cm3 in the patient group. The most frequent accompanying
pathologies were tracheal diverticulum, bronchiectasis and pulmonary artery enlargement.
Conclusion: In patients with MKS, there is a significant difference in volume calculation as in
trachea diameter. Though bronchiectasis and tracheal diverticulum are known as pathologies most
frequently accompanying MKS, to the knowledge of the researchers, pulmonary artery enlargement
due to the increase in pulmonary truncus diameter was first emphasized in this article.