Management of Connective Tissue Interstitial Lung Disease

Author(s): Tracy M. Frech, Mary Beth Scholand

Journal Name: Current Respiratory Medicine Reviews

Volume 11 , Issue 2 , 2015

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The connective tissue diseases (CTD) are frequently associated with Interestitial lung diseases (ILD). The presence of an ILD in a patient with CTD is associated with a higher morbidity and mortality. Management of a patient with connective tissue interstitial lung disease (CTD-ILD) depends on disease severity with a focus on improving quality of life. Therapeutic interventions include medications, which aim to prevent progression to fibrosis and decrease inflammation or alveolitis, supplemental oxygen; and pulmonary rehabilitation. Comorbidities including gastroesophageal reflux disease (GERD) and obstructive sleep apnea should be addressed in all CTD-ILD patients. Appropriate referral to support groups, lung transplantation centers, and palliative care are considerations for all patients with CTDILD. The management of a patient with CTD-ILD is a multidisciplinary personalized process that is driven by the specific disease, clinical pattern, and associated comorbidities.

Keywords: Collagen vascular disease, connective tissue disease, immunosuppressive therapy, interstitial lung disease, oxygen, pulmonary rehabilitation, supportive care.

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Article Details

Year: 2015
Published on: 30 August, 2015
Page: [150 - 155]
Pages: 6
DOI: 10.2174/1573398X11666150619183704
Price: $65

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