Alveolar Capillary Dysplasia: A Lethal Developmental Lung Malformation

Author(s): Aaron W. Swenson, Steven M. Donn.

Journal Name: Current Respiratory Medicine Reviews

Volume 5 , Issue 2 , 2009

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Abstract:

Alveolar capillary dysplasia (ACD) is a recently recognized lethal lung malformation. ACD is a rare congenital disorder of pulmonary vascular development associated with unremitting hypoxemia and respiratory failure. This paper reviews the incidence, pathophysiology and histopathology, clinical manifestations, diagnosis, and treatment of affected newborns and proposes an algorithmic approach to management of infants who present with unremitting persistent pulmonary hypertension of the newborn.

Keywords: Newborn, alveolar capillary dysplasia, pulmonary hypertension, extracorporeal membrane oxygenation

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Article Details

VOLUME: 5
ISSUE: 2
Year: 2009
Page: [110 - 114]
Pages: 5
DOI: 10.2174/157339809788189950
Price: $58

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