Two Cases of Glucose-6-phosphate Dehydrogenase Deficiency Presenting as Symptomatic Methemoglobinemia with Persistently Low Saturations After Fava Bean Ingestion in United Arab Emirates
Majid Al Teneiji,
Muhammad Faisal Khanani,
Layla Al Reyami,
Najam Ahmed Awan.
We report two cases of one previously healthy child and another known to
have G6PD deficiency, who presented with desaturation despite their stable clinical
appearance, which later was attributed to methemoglobinemia (MetHb) that was precipitated
by fava beans ingestion.
When hemolytic crisis occurs, certain G6PD deficient patients might develop cyanosis
and show evidence of concurrent methemoglobinemia.
In conclusion, Methemoglobinemia is a rare but important cause of persistently low
Keywords: Acute hemolysis, Favism, Glucose-6-phosphate dehydrogenase deficiency, Methemoglobinemia.
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