Management of Connective Tissue Interstitial Lung Disease
Tracy M. Frech,
Mary Beth Scholand.
The connective tissue diseases (CTD) are frequently associated with Interestitial lung diseases (ILD). The
presence of an ILD in a patient with CTD is associated with a higher morbidity and mortality. Management of a patient
with connective tissue interstitial lung disease (CTD-ILD) depends on disease severity with a focus on improving quality
of life. Therapeutic interventions include medications, which aim to prevent progression to fibrosis and decrease
inflammation or alveolitis, supplemental oxygen; and pulmonary rehabilitation. Comorbidities including gastroesophageal
reflux disease (GERD) and obstructive sleep apnea should be addressed in all CTD-ILD patients. Appropriate
referral to support groups, lung transplantation centers, and palliative care are considerations for all patients with CTDILD.
The management of a patient with CTD-ILD is a multidisciplinary personalized process that is driven by the specific
disease, clinical pattern, and associated comorbidities.
Keywords: Collagen vascular disease, connective tissue disease, immunosuppressive therapy, interstitial lung disease, oxygen,
pulmonary rehabilitation, supportive care.
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